3-Hydroxyglutaric Acid
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产品名称:
3-Hydroxyglutaric Acid
产品型号:
GOY-Y0259
产品展商:
谷研
产品文档:
无相关文档
发布时间:2023-04-10
简单介绍
3-Hydroxyglutaric AcidDMF: 30 mg/ml,DMSO: 30 mg/ml,Ethanol: 30 mg/ml,PBS (pH 7.2): 10 mg/ml
3-Hydroxyglutaric Acid
的详细介绍
性能参数
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产品名称
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3-Hydroxyglutaric Acid
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规格
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1mg 5mg 10mg 25mg
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货号
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GOY-Y0259
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含量
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>95.00%
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CAS
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638-18-6
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别名
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N/A
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化学名
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N/A
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分子式
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C5H8O5
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分子量
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分子 148.1
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溶解度
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DMF: 30 mg/ml,DMSO: 30 mg/ml,Ethanol: 30 mg/ml,PBS (pH 7.2): 10 mg/ml
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储存条件
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Store at -20°C
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General tips
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用途
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仅供科研
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价格
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电询
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详细内容
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Glutaryl-CoA dehydrogenase (GCDH) is a mitochondrial matrix protein that catalyzes the oxidative decarboxylation of glutaryl-CoA to crotonyl-CoA and carbon dioxide in the catabolic pathways of lysine, hydroxylysine, and tryptophan metabolism. 3-Hydroxyglutaric acid is one of several metabolites produced when insufficient levels of GCDH are available. Urinary levels of 3-hydroxyglutaric acid are elevated during glutaric acidemia type 1, an autosomal recessive GCDH deficiency disorder that can lead to neurodegeneration if left untreated. 3-Hydroxyglutaric acid is used as a biomarker of GCDH deficiency.
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