商品属性:
产品名称 |
ACOX1抗体 |
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英文名称 |
ACOX1 |
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产品规格 |
50ul 100ul 200ul |
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产品货号 |
GOY-01K0181 |
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产品分类 |
抗体 / 一抗 |
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交叉反应 |
Human, Mouse, Rat, Pig, Rabbit, Sheep |
保存条件 |
Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles. |
标记 |
Unconjugated |
抗体来源 |
Rabbit |
抗体类型 |
Polyclonal |
研究领域 |
肿瘤 细胞生物 转录调节因子 |
蛋白细胞定位 |
细胞浆 |
纯化方法 |
affinity purified by Protein A |
性状 |
Liquid |
浓度 |
1mg/ml |
储存液 |
0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol. |
发货地 |
上海 |
背景资料 |
Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD); also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning. |
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传真号码:021-39596320 021-39921927
QQ: 3004918891 3004905818 3004901493
移动电话:18321818584 15026555973
地址:上海松江新砖公路1155号
产品均为实验试剂,仅供科研实验使用,非药品、非食品、不可用于动物及人体!