产品名称

GCSH抗体

英文名称

GCSH

产品规格

50ul  100ul 200ul 

产品货号

GOY-01K4507

产品分类

抗体 / 一抗

交叉反应

Human, Mouse, Rat, Horse

保存条件

Shipped at 4℃. Store at -20 °C for one year. Avoid repeated freeze/thaw cycles.

标记

Unconjugated

抗体来源

Rabbit

抗体类型

Polyclonal

研究领域

蛋白细胞定位

细胞浆

纯化方法

affinity purified by Protein A

性状

Liquid

浓度

1mg/ml

储存液

0.01M TBS(pH7.4) with 1% BSA, 0.03% Proclin300 and 50% Glycerol.

发货地

上海

背景资料

GCSH is a 173 amino acid mitochondrial protein that contains one lipoyl-binding domain and belongs to the gcvH family. Defects in the e encoding GCSH are the cause of glycine encephalopathy (GCE), an autosomal recessive disease that is also referred to as?